Biochimica et Biophysica Acta (BBA) - Molecular Cell Research
Volume 1793, Issue 4, April 2009, Pages 674-683
ReviewPrinciples of lysosomal membrane degradation: Cellular topology and biochemistry of lysosomal lipid degradation
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Abbreviations
BMP
bis(monoacylglycero)phosphate
CADs
cationic amphiphilic drugs
GlcCer
glucosylceramide
GM3
NeuAcα2,3Galβ1,4Glcβ1ceramide
GM2
GalNAcβ1,4(NeuAcα2,3)Galβ1,4Glcβ1ceramide
GM2-AP
GM2 activator protein
GSL
glycosphingolipids
LLBP
lysosomal lipid binding proteins
MVBs
multivesicular bodies
NPC
Niemann–Pick disease Type C
SAPs
sphingolipid activator proteins (Sap A–D and GM2-AP)
Sap
saposin A–D
Keywords
Lysosome
Glycosphingolipid
Sphingolipid activator protein
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